Malignant Peripheral Nerve Sheath Tumor
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Malignant peripheral nerve sheath tumor
- Malignant peripheral nerve sheath tumors are rare, high-grade, soft-tissue sarcoma that typically arise from Schwann cells and typically occur in adults (more so than children).
- They are locally invasive and often present as an enlarging mass.
- They can arise from malignant transformation of a plexiform neurofibroma, thus they have a strong association with Neurofibromatosis, Type 1.
References
- Adesina, Adekunle M., Tarik Tihan, Christine E. Fuller, and Tina Young Poussaint. Atlas of Pediatric Brain Tumors. Springer, 2016.
- Bockenheimer, Ph (Philipp). Atlas of Clinical Surgery; with Special Reference to Diagnosis and Treatment for Practitioners and Students. New York?: Rebman, 1908. http://archive.org/details/atlasofclinicals00bock.
- Gray, Frangoise, Charles Duyckaerts, and Umberto De Girolami. Escourolle and Poirier’s Manual of Basic Neuropathology. OUP USA, 2013.
- Newton, Herbert B. Handbook of Brain Tumor Chemotherapy, Molecular Therapeutics, and Immunotherapy. Academic Press, 2018.
- Orkin, Stuart H., David E. Fisher, A. Thomas Look, Samuel Lux, David Ginsburg, and David G. Nathan. Oncology of Infancy and Childhood E-Book. Elsevier Health Sciences, 2009.
Image Reference
- Malignant peripheral nerve sheath tumor of left tibia
- “Cases Journal.” Cases Journal. Accessed July 16, 2018. https://casesjournal.biomedcentral.com/.